---

Susac syndrome: A rare presentation

---

Case Report

Author Details : Imtiyaz Ahmad Lone, Ourfa Ashraf Wani*

Volume : 8, Issue : 2, Year : 2022

Article Page : 311-313

https://doi.org/10.18231/j.ijceo.2022.063

Suggest article by email

Get Permission

---

Abstract

Susac syndrome is an autoimmune microangiopathy characterized by a triad of encephalopathy, sensori-neural hearing loss and varying degrees of branch retinal artery occlusion. A young male patient is described with features of focal neurological lesions and small superficial retinal haemorrhages and areas of retinal arteriolar endothelial inflammation appearing as Gass plaques. Susac syndrome presents with varying features involving brain, inner ear and retina. Fundus Fluorescein angiography should be performed in all patients with an unexplained encephalopathy to look for characteristic arteriolar wall changes.
 

Keywords: Susac Syndrome, Branch retinal artery occlusion, Gass plaques, Encephalopathy

How to cite : Lone I A, Wani O A, Susac syndrome: A rare presentation. Indian J Clin Exp Ophthalmol 2022;8(2):311-313

This is an Open Access (OA) journal, and articles are distributed under the terms of the Creative Commons Attribution-NonCommercial-ShareAlike 4.0 License, which allows others to remix, tweak, and build upon the work non-commercially, as long as appropriate credit is given and the new creations are licensed under the identical terms.